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Transient Familial Hyperbilirubinemia





Transient Familial Hyperbilirubinemia

Definition:

Transient familial hyperbilirubinemia is an inherited metabolic disorder. Babies with this disorder are born with severe jaundice.


Alternative Names:
Lucey-Driscol Syndrome
Causes, incidence, and risk factors:

Transient familial hyperbilirubinemia is thought to be an autosomal recessive inherited disorder.It occurs when the body does not properlybreak down (metabolize) bilirubin. Bilirubin levelsrapidly build up in the body. These high levels arepoisonous to the brain and can cause death.





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