Saturday, May 26, 2012

Incontinentia pigmenti syndrome

Table of Contents

Alternative Names

Bloch-Sulzberger syndrome


Treatment

There is no specific treatment for IP. Treatment is aimed at the individual symptoms. For example, glasses may be needed to improve vision. Medicine may be prescribed to help control seizures or muscle spasms.


Support Groups


Expectations (prognosis)

How well a person does depends on the severity of central nervous system involvement and eye problems.


Complications
  • Delayed development
  • Infections of blistered skin
  • Mental retardation
  • Muscle spasticity
  • Paralysis
  • Seizures
  • Walking difficulty
  • Vision problems

Calling your health care provider

Call your health care provider if:

  • You have a family history of IP and are considering having children
  • Your child has symptoms of this disorder


Review Date: 05/13/2011
Reviewed By: Kevin Berman, MD, PhD, Atlanta Center for Dermatologic Disease, Atlanta, GA. Review provided by VeriMed Healthcare Network.  Also reviewed by David Zieve, MD, MHA, Medical Director, A.D.A.M., Inc.

A.D.A.M., Inc. is accredited by URAC, also known as the American Accreditation HealthCare Commission (www.urac.org)