Thursday, February, 09, 2012

Aminoaciduria

Table of Contents

Alternative Names

Amino acids - urine; Urine amino acids


Normal Values

The specific value is measured in micromoles per deciliter (micromol/dL).

  • Alanine
    • Children: 65 to 190
    • Adults: 160 to 690
  • Alpha-aminoadipic acid
    • Children: 25 to 78
    • Adults: 0 to 165
  • Alpha-amino-N-butyric acid
    • Children: 7 to 25
    • Adults: 0 to 28
  • Arginine
    • Children: 10 to 25
    • Adults: 13 to 64
  • Asparagine
    • Children: 15 to 40
    • Adults: 34 to 100
  • Aspartic acid
    • Children: 10 to 26
    • Adults: 14 to 89
  • Beta-alanine
    • Children: 0 to 42
    • Adults: 0 to 93
  • Beta-amino-isobutyric acid
    • Children: 25 to 96
    • Adults: 10 to 235
  • Carnosine
    • Children: 34 to 220
    • Adults: 16 to 125
  • Citrulline
    • Children: 0 to 13
    • Adults: 0 to 11
  • Cystine
    • Children: 11 to 53
    • Adults: 28 to 115
  • Glutamic acid
    • Children: 13 to 22
    • Adults: 27 to 105
  • Glutamine
    • Children: 150 to 400
    • Adults: 300 to 1,040
  • Glycine
    • Children: 195 to 855
    • Adults: 750 to 2,400
  • Histidine
    • Children: 46 to 725
    • Adults: 500 to 1,500
  • Hydroxyproline
    • Children: not measured
    • Adults: not measured
  • Isoleucine
    • Children: 3 to 15
    • Adults: 4 to 23
  • Leucine
    • Children: 9 to 23
    • Adults: 20 to 77
  • Lysine
    • Children: 19 to 140
    • Adults: 32 to 290
  • Methionine
    • Children: 7 to 20
    • Adults: 5 to 30
  • 1-methylhistidine
    • Children: 41 to 300
    • Adults: 68 to 855
  • 3-methylhistidine
    • Children: 42 to 135
    • Adults: 64 to 320
  • Ornithine
    • Children: 3 to 16
    • Adults: 5 to 70
  • Phenylalanine
    • Children: 20 to 61
    • Adults: 36 to 90
  • Phosphoserine
    • Children: 16 to 34
    • Adults: 28 to 95
  • Phosphoethanolamine
    • Children: 24 to 66
    • Adults: 17 to 95
  • Proline
    • Children: not measured
    • Adults: not measured
  • Serine
    • Children: 93 to 210
    • Adults: 200 to 695
  • Taurine
    • Children: 62 to 970
    • Adults: 267 to 1,290
  • Threonine
    • Children: 25 to 100
    • Adults: 80 to 320
  • Tyrosine
    • Children: 30 to 83
    • Adults: 38 to 145
  • Valine
    • Children: 17 to 37
    • Adults: 19 to 74

What abnormal results mean

Increased total urine amino acids may be due to:

  • Alkaptonuria
  • Canavan disease
  • Cystinosis
  • Cystathioninuria
  • Fructose intolerance
  • Galactosemia
  • Hartnup disease
  • Homocystinuria
  • Hyperammonemia
  • Hyperparathyroidism
  • Maple syrup urine disease
  • Methylmalonic acidemia
  • Multiple myeloma
  • Ornithine transcarbamylase deficiency
  • Osteomalacia
  • Propionic acidemia
  • Rickets
  • Tyrosinemia type 1
  • Tyrosinemia type 2
  • Viral hepatitis
  • Wilson's disease


Review Date: 05/12/2011
Reviewed By: Frank A. Greco, M.D., Ph.D., Director, Biophysical Laboratory, The Lahey Clinic, Burlington, MA. Review provided by VeriMed Healthcare Network. Also reviewed by David Zieve, MD, MHA, Medical Director, A.D.A.M., Inc.

A.D.A.M., Inc. is accredited by URAC, also known as the American Accreditation HealthCare Commission (www.urac.org)