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Pulmonary alveolar proteinosis

  • Alternative Names

    Alveolar proteinosis; Pulmonary alveolar phospholipoproteinosis


    Treatment

    Treatment involves washing out the protein substance from the lung (whole-lung lavage) from time to time. Certain patients with this disease may need to have a lung transplant.

    Research has shown some benefit to an experimental treatment that uses a blood-stimulating medication called granulocyte-macrophage colony stimulating factor (GM-CSF), which is known to be lacking in some patients with alveolar proteinosis.


    Support Groups


    Expectations (prognosis)

    Some people with this condition go into remission. Others have respiratory failure that gets worse, and they may need a lung transplant. Up to 25% of people with this condition die within 5 years of being diagnosed.


    Complications


    Calling your health care provider

    Call your health care provider if you develop serious breathing symptoms. Shortness of breath that gets worse over time may signal that your condition is developing into a more serious medical emergency.