Symptoms often first appear in childhood, but severe vision problems do not usually develop until early adulthood.
- Decreased vision at night or in low light
- Loss of side (peripheral) vision, causing "tunnel vision"
- Loss of
centralvision (in advanced cases)
Signs and tests
Tests to evaluate the retina:
- Color vision
- Examination of the retina by
ophthalmoscopyafter the pupils have been dilated Fluorescein angiography Intraocular pressure
- Measurement of the electrical activity in the retina (
- Pupil reflex response
Refraction test Retinal photography
- Side vision test (visual field test)
Slit lamp examination Visual acuity